3.2 of 13 Ratings
Figure A is a clinical photo of a 2 year old male with a right hand abnormality. In addition to his right hand deformity, he has a similar appearance of his left hand. He also has a cleft palate, craniofacial defects, and bilateral club feet. His upper extremities are otherwise normal proximal to his wrists. The diagnosis was suspected after a routine ultrasound. What is the inheritance pattern of this condition?
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Figure A depicts a child with a congenital abnormality. Which of the following is true regarding this condition?
Circumferential trunk involvement is more common than distal extremities involvement
Risk factors include late gestation (>44 weeks) and high birth weight (>3500g)
Incomplete circumferential bands not directly interfering with lymphatic circulation should be resected
There is a strong correlation with anterolateral tibial bowing
Complete circumferential bands that interfere with lymphatic drainage can be treated with band excision and z-plasty.