Please confirm topic selection

Are you sure you want to trigger topic in your Anconeus AI algorithm?

Please confirm action

You are done for today with this topic.

Would you like to start learning session with this topic items scheduled for future?

Updated: May 22 2021

Poland Syndrome

Images syndrome.jpg[1]_moved.gif[1]_moved.jpg
  • Introduction
    • A congenital disorder characterized by
      • unilateral chest wall hypoplasia
        • due to absence of sternocostal head of pectoralis major
      • hypoplasia of the hand and forearm
      • symbrachydactyly and shortening of middle fingers
        • result of absence or shortening of the middle phalanx
        • simple complete syndactyly of the short digits
  • Epidemiology
    • Incidence
      • 1 in 32,000 live births
  • Etiology
    • Pathophysiology
      • thought to be linked to subclavian artery hypoplasia
    • Associated conditions
      • occurs in 10% of syndactyly cases
  • Presentation
    • Physical exam
      • extent of hand and chest involvement varies
      • chest deformities
        • hypoplasia or absence of the pectoralis major, pectoralis minor, deltoid, serratus anterior, external oblique, and latissimus dorsi
        • Sprengel’s deformity
        • scoliosis
        • dextrocardia
        • absence or underdevelopment of the breast
      • hand deformities
        • syndactyly
        • hypoplasia or absence of metacarpals or phalanges
        • absence of extensors or flexor tendons
        • carpal coalition or hypoplasia
        • radioulnar synostosis
        • nail agenesis
  • Imaging
    • CT scan
      • will show absent perctoralis major
  • Treatment
    • Operative
      • syndactyly release
        • indications
          • performed in most patients
        • technique
          • complete syndactyly release produces skin deficiency that requires skin grafting
          • perform only one side of the digit at a time to avoid vascular complications
          • local flap is created for commisure reconstruction followed by interdigitating zigzag dorsal and palmar flaps along the medial and lateral aspect of the digit
  • Complications
    • Skin graft failure
    • Excessive tension
    • Improper flap planning
    • Digital artery injury
    • Web creep
    • Nail deformity
1 of 1
1 of 4
Private Note

Attach Treatment Poll
Treatment poll is required to gain more useful feedback from members.
Please enter Question Text
Please enter at least 2 unique options
Please enter at least 2 unique options
Please enter at least 2 unique options