Updated: 1/30/2020

Local Gigantism

0%
Topic
Review Topic
0
0
N/A
N/A
Questions
1
0
0
0%
0%
Evidence
1
0
0
Topic
https://upload.orthobullets.com/topic/4083/images/local_gigantism_moved.jpg
Introduction
  • Overview
    • form of gigantism usually isolated to fingers or toes "macrodactyly" but may affect an entire limb
  • Epidemiology & Incidence
    • rare
    • congenital causes:
      • neurofibromatosis
      • proteus syndrome
      • klippel-Trenaunay-Weber
    •  acquired causes:
      • amyloidosis
      • elephantiasis (filariasis)
      • av malformation
      • tumor
      • acromegaly
  • Physiology
    • unknown
Relevant Anatomy
  • Growth plate consists of three principal layers:
    • resting zone
    • proliferative zone
    • hypertrophic zone
Presentation
  • Symptoms
    • pain
  • Physical exam
    • enlarged digit or limb
Imaging
  • Radiograhs
    • needed for reconstruction or amputation planning
Treatment
  • Nonoperative
    • observation
      • monitor growth of affected region
  • Operative
    • epiphysiodesis vs. bony and soft-tissue reduction procedures
      • indications
        • individualized based on etiology, location of affected area, skeletal growth left, and severity
    • amputation 

Please rate topic.

Average 2.2 of 18 Ratings

Questions (1)
Question locked
Sorry, this question is for
PEAK Premium Subscribers only
Upgrade to PEAK
Evidence (1)
EXPERT COMMENTS (0)
Private Note