| Introduction |
 Overview
- form of gigantism usually isolated to fingers or toes "macrodactyly" but may affect an entire limb
- Epidemiology & Incidence
- rare
- congenital causes:
- neurofibromatosis
- proteus syndrome
- klippel-Trenaunay-Weber
- acquired causes:
- amyloidosis
- elephantiasis (filariasis)
- av malformation
- tumor
- acromegaly
- Physiology
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| Relevant Anatomy |
- Growth plate consists of three principal layers:
- resting zone
- proliferative zone
- hypertrophic zone
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| Presentation |
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| Imaging |
- Radiograhs
- needed for reconstruction or amputation planning
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| Treatment |
- Nonoperative
- monitor growth of affected region
- Operative
- individualized based on etiology, location of affected area, skeletal growth left, and severity
- soft-tissue debulking
- epiphysiodesis of affected phalanges
- bony and soft-tissue reduction procedures
- amputation
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