QUESTIONS 1 of 11 1 2 3 4 5 6 7 8 9 10 11 Previous Next Sorry, this question is for PEAK Premium Subscribers only Upgrade to PEAK (OBQ19.156) Figures A&B are the radiographs of a 5-year-old male who presents for evaluation of right lower leg pain. On examination, he is noted to have freckling in the axilla and optic examination is seen in Figure C. What is the pattern of inheritance of this most likely disease? QID: 214058 FIGURES: A B C Type & Select Correct Answer 1 Autosomal dominant 84% (874/1040) 2 Autosomal recessive 10% (105/1040) 3 Non-inherited 1% (9/1040) 4 X-linked dominant 1% (14/1040) 5 X-linked recessive 3% (33/1040) L 2 Question Complexity A Question Importance Select Answer to see Preferred Response SUBMIT RESPONSE 1 Review Tested Concept Review Full Topic (OBQ18.38) A child is found to have axillary and inguinal freckling, scoliosis, and hamartomas within his iris. Which of the following pairs the inheritance pattern of the condition with the leg abnormality found in the condition? QID: 212934 FIGURES: A B C Type & Select Correct Answer 1 Autosomal dominant; Figure B 73% (1364/1867) 2 Autosomal recessive; Figure B 12% (217/1867) 3 X-linked recessive; Figure A 4% (66/1867) 4 Autosomal dominant; Figure C 6% (105/1867) 5 Autosomal recessive; Figure A 6% (103/1867) L 2 Question Complexity A Question Importance Select Answer to see Preferred Response SUBMIT RESPONSE 1 Review Tested Concept Review Full Topic (OBQ18.49) A 6-year-old boy with neurofibromatosis type 1 returns for follow-up of the condition shown in Figures A and B. The patient has attempted bracing with a knee-ankle-foot orthosis and long leg casting but has not had any radiographic improvement. What is the best next step in management? QID: 212945 FIGURES: A B Type & Select Correct Answer 1 Continued bracing 6% (114/1985) 2 Bone stimulator 2% (39/1985) 3 Intramedullary nailing 4% (84/1985) 4 Resection of pseudoarthrosis , bone grafting, and intramedullary nailing 86% (1717/1985) 5 Amputation 1% (18/1985) L 2 Question Complexity A Question Importance Select Answer to see Preferred Response SUBMIT RESPONSE 4 Review Tested Concept Review Full Topic (SBQ13PE.55) A 4-year-old boy is referred to your office for evaluation of a progressive lower extremity deformity. AP radiographs are shown in Figure A. All of the following may also be found on physical examination EXCEPT: QID: 5127 FIGURES: A B C D E F Type & Select Correct Answer 1 Figure B 7% (132/1814) 2 Figure C 5% (88/1814) 3 Figure D 4% (73/1814) 4 Figure E 76% (1385/1814) 5 Figure F 7% (128/1814) N/A Question Complexity B Question Importance Select Answer to see Preferred Response SUBMIT RESPONSE 4 Review Tested Concept Review Full Topic Sorry, this question is for PEAK Premium Subscribers only Upgrade to PEAK Sorry, this question is for PEAK Premium Subscribers only Upgrade to PEAK (OBQ08.37) A 3-year-old boy presents with a forearm deformity. Radiographs are shown in Figure A. Ophthalmologic exam shows the lesion seen in Figure B. These finding are most consistent with which of the following conditions? QID: 423 FIGURES: A B Type & Select Correct Answer 1 Achondroplasia 0% (3/1637) 2 Fibrous dysplasia 2% (29/1637) 3 Osteogenesis imperfecta 8% (134/1637) 4 Neurofibromatosis Type 1 86% (1416/1637) 5 Ollier's disease 3% (45/1637) L 1 Question Complexity C Question Importance Select Answer to see Preferred Response SUBMIT RESPONSE 4 Review Tested Concept Review Full Topic (OBQ06.202) A 3-year-old boy presents with the skin lesion seen in Figure A and a leg deformity. Radiographs are shown in Figure B. What is the most appropriate first step in treatment? QID: 213 FIGURES: A B Type & Select Correct Answer 1 observation 21% (610/2897) 2 bracing in total contact orthosis 73% (2101/2897) 3 intramedullary nailing with bone grafting 3% (81/2897) 4 free fibular graft from contralateral side 1% (15/2897) 5 external fixation using Illizarov techniques 3% (73/2897) L 2 Question Complexity C Question Importance Select Answer to see Preferred Response SUBMIT RESPONSE 2 Review Tested Concept Review Full Topic (OBQ05.43) The diagnostic criteria for neurofibromatosis type I includes all of the following EXCEPT: QID: 79 Type & Select Correct Answer 1 2 or more neurofibromas 1% (19/1357) 2 6 or more cafe-au-lait macules 2% (25/1357) 3 2 or more Lisch nodules 3% (37/1357) 4 freckling on the plantar surface of the feet 82% (1109/1357) 5 optic glioma 12% (164/1357) L 2 Question Complexity C Question Importance Select Answer to see Preferred Response SUBMIT RESPONSE 4 Review Tested Concept Review Full Topic (SBQ04PE.41) A 3-year-old male is evaluated in your office. On examination he is found to have several pigmented cutaneous lesions and hamartomas of the iris. His right leg was previously treated with both a knee-ankle-foot orthotic and long-leg casting for approximately 9 months. His most recent radiographs are seen in Figures A and B. What is the next best treatment? QID: 2226 FIGURES: A B Type & Select Correct Answer 1 Bone stimulator 2% (37/1897) 2 Continue bracing 8% (159/1897) 3 Syme amputation 1% (12/1897) 4 Resection of pseudoarthrosis with bone grafting and surgical fixation 87% (1657/1897) 5 Below knee amputation 1% (25/1897) L 2 Question Complexity C Question Importance Select Answer to see Preferred Response SUBMIT RESPONSE 4 Review Tested Concept Review Full Topic