summary Juvenile Idiopathic Scoliosis is a coronal plane spinal deformity which most commonly presents in children between ages 4 and 10. Diagnosis is made with full-length standing PA and lateral spine radiographs. MRI studies are indicated in children <10 years old with a curve > 20°. Treatment can be observation, bracing, or surgical management depending on the skeletal maturity of the patient, magnitude of deformity, and curve progression. Epidemiology Incidence 15% of all idiopathic scoliosis cases Demographics females > males Anatomic location most commonly appear as a right main thoracic curve Etiology Associated conditions high incidence of neural axis abnormalities (18-25%) syringomyelia cyst or tubular cavity within spinal cord can be seen in a scoliotic curve without rotation can manifest as an asymmetric umbilicus reflex Arnold-Chiari syndrome cerebellar tonsil are elongated and protruding through the opening of the base of the skull and blocking CSF flow) tethered cord dysraphism spinal cord tumor Classification Early onset scoliosis (EOS) early-onset scoliosis is a broader category including scoliosis in children <10 years old. It includes infantile idiopathic scoliosis juvenile idiopathic scoliosis congenital scoliosis neurogenic scoliosis syndromic scoliosis Marfan's Down's syndrome Presentation History important to determine when deformity was first noticed and any observed progression get perinatal history Presentation failure to develop bowel and bladder control by age ~ 3 or 4 may indicate neurologic involvement patients often referred from school screening where a 7° curve on scoliometer during Adams forward bending test is considered abnormal 7° correlates with 20° coronal plane curve Physical exam general inspection cafe-au-lait spots (neurofibromatosis) leg length inequality shoulder height differences truncal shift waist asymmetry and pelvic tilt foot deformities (cavovarus) can suggest neural axis abnormalities and warrant a MRI spine inspection midline skin defects hairy patches dimples (signs of spinal dysraphism) nevi rib rotational deformity (rib prominence) Adams forward bending test axial plane deformity indicates structural curve forward bending sitting test can eliminate leg length inequality as cause of scoliosis neurologic motor upper and lower extremities exam reflexes abnormal abdominal reflexes associated with the presence of a syrinx gently stroking each abdominal quadrant should cause contraction of the abdominal muscles clonus Hoffman sign Babinski gait analysis Imaging Radiographs PA and lateral upright images are used to assess curve severity treatment based on Cobb angle Cobb angle > 10° defined as scoliosis intra-interobserver error of 3-5° bending radiographs can help determine which curves require fusion MRI indicated in children <10 years old with a curve > 20° even in the absence of neurologic symptoms must rule out neural axis abnormalities (e.g., syringomyelia) presence of left-sided thoracic curve Treatment Nonoperative observation indications curves < 20° technique frequent radiographs to observe for curve progression bracing indications curves 20 - 50° designed to prevent curve progression, not correct the curve relative contraindication to bracing is thoracic hypokyphosis technique 16-23h/day until skeletal growth completed or surgery indicated Operative non-fusion procedures (growing rods, VEPTR) indications curves > 50° in small children with significant growth remaining allows continued spinal growth over unfused segments definitive PSF + ASF performed when the child has grown and is closer skeletal maturity traditional growing rods associated with greater curve correction and truncal height gain than VEPTR constructs anterior / posterior spinal fusion indications curves > 50° in younger patients required in order to prevent crankshaft phenomenon posterior spinal fusion indications curve > 50° in older patients near skeletal maturity remains gold standard for thoracic and double major curves (most cases) anterior spinal fusion indications curve > 50° best for thoracolumbar and lumbar cases with a normal sagittal profile Complications Crankshaft phenomenon Prognosis High risk of progression 70% require treatment (50% bracing, 50% surgery) Very few experience spontaneous resolution Can be fatal if not treated appropriately
Technique Guide Technique guides are not considered high yield topics for orthopaedic standardized exams including ABOS, EBOT and RC. Anterior Spinal Fusion Lindsay Andras David L. Skaggs Spine - Juvenile Idiopathic Scoliosis Technique Guide Technique guides are not considered high yield topics for orthopaedic standardized exams including ABOS, EBOT and RC. Growing Rod Instrumentation Lindsay Andras David L. Skaggs Spine - Juvenile Idiopathic Scoliosis
QUESTIONS 1 of 8 1 2 3 4 5 6 7 8 Previous Next Sorry, this question is for PEAK Premium Subscribers only Upgrade to PEAK Sorry, this question is for PEAK Premium Subscribers only Upgrade to PEAK (OBQ18.40) A thin 8-year-old patient presents for scoliosis follow-up. The patient denies experiencing any back pain and has been participating in sports. Neurologic exam of the lower extremities is normal. Lightly brushing each abdominal quadrant does not cause the umbilicus to move in any direction. Radiographs from 1 year ago are shown in Figures A and B. Radiographs from today are shown in figures C and D. What is potentially concerning and what is the best next step? QID: 212936 FIGURES: A B C D Type & Select Correct Answer 1 Curve progression; correction with growing rods 20% (457/2301) 2 Pulmonary compromise; posterior spinal fusion 3% (64/2301) 3 Curve progression; 24-hour per day bracing 20% (450/2301) 4 Spinal cord abnormalities; MRI of the entire spine 57% (1311/2301) 5 Progressive pelvic tilt; anterior and posterior spinal fusion 0% (5/2301) L 3 Question Complexity A Question Importance Select Answer to see Preferred Response SUBMIT RESPONSE 4 Review Tested Concept Review Full Topic (SBQ13PE.50) A 7 year-old boy is referred to your office for evaluation of scoliosis. All of the following are indications to obtain a screening MRI EXCEPT: QID: 5107 Type & Select Correct Answer 1 Male gender 34% (807/2367) 2 Age younger than 11 5% (111/2367) 3 Absence of thoracic apical segment lordosis on clinical exam 9% (210/2367) 4 Right thoracic curve on AP radiograph 50% (1179/2367) 5 Hyperreflexia and decreased sensation over bilateral forearms and flanks 2% (46/2367) L 4 Question Complexity C Question Importance Select Answer to see Preferred Response SUBMIT RESPONSE 4 Review Tested Concept Review Full Topic Sorry, this question is for PEAK Premium Subscribers only Upgrade to PEAK Sorry, this question is for PEAK Premium Subscribers only Upgrade to PEAK Sorry, this question is for PEAK Premium Subscribers only Upgrade to PEAK Sorry, this question is for PEAK Premium Subscribers only Upgrade to PEAK
All Videos (125) Podcasts (1) Login to View Community Videos Login to View Community Videos 2019 Orthopaedic Summit Evolving Techniques Current New Scoliosis Surgical Management Techniques - Suken H Shah, MD, MHCDS Spine - Juvenile Idiopathic Scoliosis C 12/2/2020 82 views 0.0 (0) The David B. Levine, MD, HSS Spine Symposium 2018 Current Controversies and Challenges in Early Onset Spinal Deformity - Suken A. Shah, MD (HSS DBL Spine 2018) Spine - Juvenile Idiopathic Scoliosis C 8/31/2020 972 views 3.0 (1) 13th International Congress on Early Onset Scoliosis - 2019 EOS Management in the Era of Spinraza? - Matthew Oetgen, MD MBA (ICEOS 2019) Spine - Juvenile Idiopathic Scoliosis C 2/10/2020 923 views 4.0 (1) Spine | Juvenille Idiopathic Scoliosis Spine - Juvenile Idiopathic Scoliosis Listen Now 12:45 min 10/16/2019 387 plays 4.8 (4) See More See Less
Juvenile Idiopathic Scoliosis (C1232) Gustavo Azevedo Spine - Juvenile Idiopathic Scoliosis E 6/23/2012 508 0 12